Pulmonary Fibrosis Support
Pulmonary Fibrosis Education

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What is Pulmonary Fibrosis (PF)?

Pulmonary Fibrosis (PF) is a chronic lung disease that affects the tissue in your lungs, causing scarring (fibrosis) over time. This scarring makes it harder for your lungs to work properly, leading to difficulty breathing and reduced oxygen levels in your bloodstream. 

Symptoms of PF

PF symptoms often develop gradually and worsen over time. Common symptoms include:

  • Shortness of breath: Initially noticeable during physical activity, it can eventually occur even at rest.
  • Chronic cough: A persistent, dry cough that doesn’t go away.
  • Fatigue: Feeling tired and worn out.
  • Unexplained weight loss: Losing weight without trying.
  • Aching muscles and joints: General discomfort in the body.
  • Clubbing: Enlargement of the fingertips or toes.

Causes and Risk Factors

The exact cause of PF is not known, but several factors may increase the risk of developing the disease:

  • Age: Most people diagnosed with PF are over 50 years old.
  • Gender: PF is more common in men than in women.
  • Smoking: A history of smoking increases the risk.
  • Genetics: Family history of PF or other lung diseases may play a role.
  • Environmental Factors: Exposure to certain dusts, chemicals, or pollutants.

Diagnosis

Diagnosing PF typically involves a combination of tests and evaluations:

  • Medical History and Physical Exam: Discussing symptoms and medical background with a healthcare provider.
  • Imaging Tests: High-resolution CT scans of the chest to look for lung scarring.
  • Lung Function Tests: Measuring how well the lungs are working.
  • Lung Biopsy: In some cases, a small sample of lung tissue may be taken for analysis.

Treatment Options

While there is no cure for PF, treatments can help manage symptoms and improve quality of life:

  • Medications: Anti-fibrotic drugs can slow the progression of lung scarring.
  • Oxygen Therapy: Supplemental oxygen can help alleviate shortness of breath.
  • Pulmonary Rehabilitation: A program of exercise and education designed to help improve lung function.
  • Lung Transplant: In severe cases, a lung transplant may be considered.

Old men playing

Living with PF

Living with PF can be challenging, but there are ways to manage the condition:

  • Stay Active: Regular, gentle exercise can help maintain lung function.
  • Healthy Diet: Eating a balanced diet can support overall health.
  • Avoid Irritants: Stay away from smoke, dust, and other lung irritants.
  • Seek Support: Connecting with support groups and counseling can provide emotional help.

Get Involved

If you or a loved one is living with PF, the Manitoba Lung Association is here to support you. We offer support groups for pulmonary fibrosis patients, family members and caregivers. Visit our Pulmonary Fibrosis Support Group page to register.